共同研究者 田口惇美(新潟大学)
研究テーマ ファブリー病モデルマウスの作製と応用

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2)Shiozuka C, Taguchi A, Matsuda J, Noguchi Y, Kunieda T, Uchio-Yamada K, Yoshioka H, Hamanaka R, Yano S, Yokoyama S, Mannen K, Kulkarni AB, Furukawa K, Ishii S: Increased globotriaosylceramide levels in a transgenic mouse expressing human. J Biochem 149, 161-17-, 2011.
3)Ishii S, Chang H-H, Yoshioka H, Shimada T, Mannen K, Higuchi Y, Taguchi A, Fan J-Q : Preclinical efficacy and safety of 1-deoxygalactonojirimycin in mice for Fabry disease. J. Pharmacol. Exp. Ther. 328, 723-731, 2009.